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VOLUME 4 , ISSUE 1 ( January-March, 2017 ) > List of Articles

CASE REPORT

A Rare Case of Intramedullary Dermoid with Atypical Presentation

Rajesh K Barooah, Abinash Dutta

Citation Information : Barooah RK, Dutta A. A Rare Case of Intramedullary Dermoid with Atypical Presentation. J Spinal Surg 2017; 4 (1):19-21.

DOI: 10.5005/jp-journals-10039-1119

Published Online: 01-03-2013

Copyright Statement:  Copyright © 2017; The Author(s).


Abstract

Background

Intraspinal dermoid cysts are rare and benign tumors that occur primarily due to the defective closure of the neural tube, an ectodermal derivative, during the process of development. They can appear subdurally, extramedullary or intramedullary, with intramedullary presentations being relatively rare.

Case presentation

We present here a 24-year-old lady with low backache radiating to both lower limbs, with tingling and numbness of both lower limbs for 3 years. MRI study of the lumbosacral spine revealed a heterogeneous intradural mass lesion in the conus medullaris region at L2-L3 level (low lying cord) displacing the traversing nerve roots. Total excision of the tumor was tone and sent for biopsy which revealed keratinocytes with keratin flakes, based on which a diagnosis of dermoid was made.

Conclusion

The intramedullary location of a primary dermoid cyst an adult is rare and thus makes this case a very unique and rare entity Keywords : dermoid cysts, intramedullary lesions, spinal cord tumours.

How to cite this article

Barooah RK, Dutta A. A Rare Case of Intramedullary Dermoid with Atypical Presentation. J Spinal Surg 2017;4(1):19-21.


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