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MGM Journal of Medical Sciences

Article Details

2017 | July-September | Issue3
CASE REPORT
Anesthetic Challenge in Corrective Hand Surgery in a Child with Russell–Silver Syndrome
Akshay K Gadre, Kasturi H Bandyopadhyay, Mumtaz Afzal, Amiya K Mishra
10.5005/jp-journals-10036-1159

ABSTRACT

Introduction: Co-morbidities associated with Russell-Silver syndrome (RSS), viz. severe postnatal growth retardation, congenital heart disease, dysmorphic facial features, limb asymmetry, various patterns of hypogonadism, and constellation of endocrine abnormalities, present significant anesthetic challenge during surgery. We report a case of Russell-Silver syndrome in a 5½-year-old boy who underwent corrective hand surgery and the anesthetic challenges he presented. Russell- Silver syndrome has an autosomal dominant inheritance pattern with variable expressivity and its diagnosis remains primarily clinical, as no definite etiology or specific tests have been established yet. We anticipated difficulty in airway management of this child and so we ensured availability of ancillary equipments and presence of skilled anesthesiologists. This helped us to conduct surgery successfully without any anesthetic complications.

Keywords: Difficult airway, Postnatal growth deficiency, Russell-Silver syndrome.

How to cite this article: Gadre AK, Bandyopadhyay KH, Afzal M, Mishra AK. Anesthetic Challenge in Corrective Hand Surgery in a Child with Russell-Silver Syndrome. MGM J Med Sci 2017;4(3):146-148.

Source of support: Nil

Conflict of interest: None

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